MOEBIUS SYNDROME IN PATIENTS WITH CLEFT LIP AND PALATE: CASE REPORT

Abstract

The Moebius syndrome or sequence of Moebius (MS), a rare, non-progressive congenital disorder of varying severity, its main manifestation unilateral or bilateral paralysis of the facial nerve, which gives inactivity of the muscles of facial expression for him innervated. Orofacial manifestations of MS are cleft palate, fissured tongue and tone the facial muscles and poor language, dental hypoplasia, drooling by the absence of lip sealing, caries, periodontal disease, micrognathia, microstomia, open bite, bifid uvula, difficulty performing excursive mandibular movements, small palpebral fissures, ptosis, bilateral epicanthus, ocular hypertelorism, deformity of the outer ear with occasional hearing loss. Patients with MS with bilateral facial paralysis present inability to smile, due to the absence of lifting the lips and labial movements, and difficulties with speech, chewing and swallowing. The aim of this study is to report the therapy in 08 years of carrier old cleft patient post foramen approach associated with Moebius syndrome attended the Oral and Maxillofacial Surgery Department of fissured center Obras Sociais Irmã Dulce (Salvador, Bahia), which showed no facial expression, eye motor deficit, absence of lip seal with drooling, microstomia, generalized gingival hyperplasia and decayed deciduous teeth. Facial paralysis and orofacial and musculoskeletal malformations presented by patients with Moebius syndrome has a number of implications for the general and oral health. The early approach of the dentist is important to the establishment of an oral condition that ensures better quality of life to the patient.